A Rare Case of Extra-Ventricular Supra-Sellar Neurocytoma – A Diagnostic Conundrum

Abstract

The brain and its associated structures are often the primary source or site of metastases for many tumors. Neurocytoma is a relatively rare neuronal neoplasm, first described as an intra-ventricular tumor that is not known to be very aggressive. It constitutes less than 0.5% of CNS neoplasms. Extraventricular Neurocytoma (EVN) is an extremely rare variant, of which only 12 cases have ever been reported in the supra-sellar region. In all of these 12 cases, the patient was initially misdiagnosed; hence, this condition is a diagnostic conundrum. Grossly, the tumor is firm and smooth with extensive blood supply and fibrous tissue. Histologically, it is similar to central Neurocytomas. This article describes a case of this extremely rare CNS tumor. We also comment on the diagnostic modalities and management.