A novel symptomatic vascular ring in a neonate

Andrea Serrao,Beniamino Tormettino,Carmela Morelli,Guido Oppido,Maria Giovanna Russo

doi:10.5348/100072z08bt2021cr

Abstract

Introduction: Vascular rings are congenital anomalies of the aortic arch system characterized by a vascular anomalies of mediastinal vessels that encircle and compress the esophagus and trachea. Aortic arch anomalies may be associated with other congenital cardiac defects or chromosomal anomalies, such as microdeletion of chromosome 22q11. In neonatal/pediatric life, clinical presentation shows stridor and difficulty in swallowing or dysphagia.

Highlights

Vascular rings are congenital anomalies of the aortic arch system characterized by a vascular anomalies of mediastinal vessels that encircle and compress the esophagus and trachea
To the best of our knowledge, we described a novel vascular ring diagnosed in fetal life and symptomatic in neonatal life
In this extremely rare case, a “true” vascular ring, like in case of double aortic arch, it is due by the left circumflex retroesophageal aortic arch, ARSA, and right patent ductus/ligamentum arteriosum

Summary

Conclusion

To the best of our knowledge, we described a novel vascular ring diagnosed in fetal life and symptomatic in neonatal life. In this extremely rare case, a “true” vascular ring, like in case of double aortic arch, it is due by the left circumflex retroesophageal aortic arch, ARSA, and right patent ductus/ligamentum arteriosum.

INTRODUCTION

Findings

DISCUSSION

CONCLUSION