“A Logical Reasoning of Spongy Myocardium”- A Case of LV Non Compaction Cardiomyopathy

Abstract

Left ventricular noncompaction cardiomyopathy (LVNC) or spongy myocardium is a rare congenital disorder prominently distinguished by deep abnormal trabeculations and intertrabecular recesses which communicate with the ventricular cavity that can be detected on Transthoracic Echocardiography (TTE) or cardiac MRI (CMR) studies. LVNC can occur in isolation or coexists with other cardiac and/or systemic anomalies and the common clinical complications are heart failure, arrhythmias, and cardio embolism. The American Heart Association classified it as a primary genetic cardiomyopathy. We described the case of a 28years old young adult who presented with heart failure for the first time. Transthoracic echocardiography showed a trabeculated, sponge-like appearance of the ventricular apical and inferolateral segments. Following evaluation with CMR imaging revealed non compaction of the left ventricle. Here we discussed the diagnosis of this case and reviewed the medical literature that concerned to LVNC.