A large left ventricular pseudoaneurysm in Behçet's disease: a case report

Seyed Mojtaba Marashi,Mohammad Hussein Mandegar,Payam Eghtesadi-Araghi

doi:10.1186/1471-2482-5-13

Seyed Mojtaba Marashi, Mohammad Hussein Mandegar + Show 1 more

Open Access

https://doi.org/10.1186/1471-2482-5-13

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Abstract

BackgroundBehçet's disease is a collagen-vascular disease most commonly seen in Asia and Mediterranean area. Different organs and systems including cardiovascular system could be involved. Pseudoaneurysm is the most common form of arterial involvement in Behçet's disease; however, cardiac pseudoaneurysm is rare.Case PresentationA rare case of 13 years old boy with a 4-year history of Behçet's disease with development of a huge left ventricular pseudoaneurysm is reported who had been admitted because of cough, chills, fever, and chest pain. Findings obtained on echocardiography, magnetic resonance imaging, chest computed tomography and coronary angiography confirmed a left ventricular pseudoaneurysm. There was no complication for next 24 months follow up period after surgical treatment.ConclusionConsidering its fatality and nonspecific manifestations, one should consider cardiac pseudoaneurysms as a potential risk in any patient with Behçet's disease.

Highlights

Behçet's disease is a collagen-vascular disease most commonly seen in Asia and Mediterranean area
In this report we present a patient with Behçet's disease and a huge left ventricular pseudoaneurysm
We have presented an unusual patient with Behçet's disease and a large (10.1 × 14.8 cm) left ventricular pseudoaneurysm

Summary

Background

In 1937, Hulusi Behçet, a Turkish dermatologist, first described a chronic autoimmune disease bearing his name with characteristic orogenital aphtous ulceration and uveitis [1]. In this report we present a patient with Behçet's disease and a huge left ventricular pseudoaneurysm. The diagnosis of Behçet's disease was established 4 years prior to this admission, that had presented with oral aphtae, orchitis, right eye uveitis leading to blindness, recurrent pseudofolliculitis, knee arthritis, and lower extremity deep vein thrombosis, all attributable to this autoimmune disorder. He had been treated by Prednisolone (15 mg/day) and Methotrexate (7.5 mg/week) for last 7 month. There was no complication for 24 months follow up period after the operation

Conclusion

Findings

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