A giant coronary artery aneurysm in a patient with Behçet's syndrome.

Abstract

A 34-year-old male was admitted to our clinic for investigating chest pain and high CRP (92 mg/l) with suspicion of Behçet’s syndrome (BS). He had a history of partially recanalized deep vein thromboses (DVT) that occurred 3 years ago in the left femoral vein and 1 year ago in the right femoral vein; recurrent oral ulceration and positive HLA-B51 testing. He did not report genital ulcers, nodular skin lesions, uveitis or other BS-associated symptoms. Pulmonary chest CT angiography did not reveal pulmonary artery involvement. Skin pathergy test and uveal examination could not be performed due to urgent coronary angiography (CA) for increasing angina pectoris. CA revealed a giant aneurysm in the left anterior descending artery (Fig. 1). A coronary artery bypass graft operation was performed after a 3-day course of methylprednisolone (1 g/day) and CYC (1000 mg i.v.) with a BS diagnosis with coronary arteritis, although he was not fulfilling BS diagnostic criteria [1].