A clinical analysis of 40 cases with congenital fibrosis of extraocular muscles

Abstract

To analyse the clinical manifestations and the effects of surgical management on Congenital fibrosis of extraocular muscles (CFEOM). Forty cases with CFEOM were retrospectively summarized. The follows were recorded and analysed, including sex, surgical age, visual acuity, refractive condition, phenotype, the diopter, the complications of eye and other position of the body, familial history, surgical methods. In the 60 eyes having refractive record, 7 eyes were simple hyperopia (11.67%), 2 eyes were simple myopia (3.33%); 51 eyes is astigmatism (85.00%); Amblyopia were 94.64%. 29 cases were CFEOM1 (72.5%); 10 cases were CFEOM 3 (25.0%); 1 case was CFEOM 2 (2.5%).10 cases had familial history (25%). The methods of surgery include recession, hang-back or tenotomy of the rectus muscles. If forced duction of the antagonist was negative, we can considered strengthening it. The clinical manifestations can be improved in 62 eyes After surgery. CFEOM is one of rare CCDDs, the astigmatism of refractive errors was among 51 eyes (85%), the incidence of amblyopia and CFEOM1 were high. The strabismic angles can be decreased in most patients through surgery.