Abstract
31Aug 2016 A CASE REPORT ON PULMONARY ALVEOLAR MICROLITHIASIS. Suman Kumar Jagaty , Pravati Dutta , Rekha Manjhi and Sudarsan Pothal. Department of pulmonary medicine, VSS Medical College, Burla, Odisha, India.
Highlights
Received: 12 June 2016 Final Accepted: 19 July 2016 Published: August 2016 error of calcium metabolism with unknown etiology and familial association in which concretions composed of calcium and phosphorus collect in alveolar spaces[1].It was first named in 1933 by Puhr
Case Report: A 42 year old male non smoker,weaver presenting with 6 months history of fever,cough with mild expectoration and dyspnea on exertion was diagnosed as miliary tuberculosis by a local physician for which he was given antitubercular treatment for 3 months but his symptoms was not improving for which he came to outdoor.He had no past history of any chronic diseases or any chronic drug use.His general physical examination was unremarkable with vitals being normal.Respiratory system examination revealed bilateral vesicular breath sound with fine inspiratory crackles in axillary,infraaxillary infrascapular area
PAM is due to inborn error of calcium metabolism confined to lung and leading to deposition of calcified spherules in alveolar spaces[2].It is inherited as autosomal recessive condition diagnosed during third through fifth decades[3].Most patients are asymptomatic.Some may present with cough,progressive dyspnea,haemoptysis.Inspiratory crackles,clubbing and signs of cor pulmonale seen in advanced cases.Chest X-ray may show diffuse micronodular shadows(sand storm pattern) and black pleura line(disease free pleura appears as black line).HRCT may show micronodular opacities and subpleural predominance.PFT may show restrictive defect[4].Transbronchial lung biopsy is confirmative[5].Currently there is no effective treatment is available except lung transplantation
Summary
Received: 12 June 2016 Final Accepted: 19 July 2016 Published: August 2016 error of calcium metabolism with unknown etiology and familial association in which concretions composed of calcium and phosphorus collect in alveolar spaces[1].It was first named in 1933 by Puhr. Case Report: A 42 year old male non smoker,weaver presenting with 6 months history of fever,cough with mild expectoration and dyspnea. Investigation: His laboratory parameters and Pulmonary function test were normal and sputum was negative for acid fast bacilli.His ABG parameter and Echocardiography report were normal.Chest X-ray shows bilateral diffuse micronodular shadows (sand-storm pattern) predominant in middle and lower zones and disease free pleura as black pleura line.HRCT thorax shows diffuse calcified micronodular opacities with lower lobe and subpleural predominance and septal thickening.BAL Fluid shows characterstic calcified spherules
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