A Case Report on Granulomatosis with Polyangitis and Diffuse Alveolar Haemorrhage

Abstract

Granulomatous polyangitis (GPA), formerly known as Wegener’s granulomatosis, is a rare form of small-vessel vasculitis. It has no gender predominance and tends to present between the ages of 40 and 55 years old in more than two-thirds of cases. GPA should be critically considered as a diagnosis when a presentation involves multiple systems, including joint, kidney, and lung. Lifesaving treatment of GPA is based on prompt and aggressive administration of pulse steroids and high doses of cyclophosphamide in repeat intervals.