Abstract
A case of pulmonary arteriovenous fistula with Osler-Weber-Rendu syndrome is described here. A 34-year-old woman was referred to the hospital because of an abnormal shadow in the lower area of the right lung. Chest tomography and CT revealed a pulmonary arteriovenous fistula located in the right middle lobe. Gastroscopy disclosed multiple mucosal telangiectases. In addition, her eldest son has an episode of rupture of spinal arteriovenous malformation. The patient was diagnosed as Osler-Weber-Rendu syndrome. Right middle lobectomy was performed. The postoperative course was uneventful. Forty-seven cases of pulmonary arteriovenous fistula with Osler-Weber-Rendu syndrome has been reported in Japan. Twenty-eight of 47 patients (60%) were females. The mean age was 34 years old and 29 patients (62%) were under 40 years old. Twenty-six patients (55%) had multiple pulmonary arteriovenous fistulas. Polycythemia was seen in 15 patients (32%) but on the contrary anemia was seen in some patients because of recurrent hemorrhage. Pulmonary arteriovenous fistula may involve brain complications such as abscess and embolism, so surgical resection should be considered, if possible.
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