A Case of Non-syndromic Craniosynostosis

Devananthan Ilenghoven,Hamidah Mohd Zainal,Normala Haji Basiron,Mohd Ali Mat Zain

doi:10.31344/ijhhs.v5i2.270

Devananthan Ilenghoven, Hamidah Mohd Zainal + Show 2 more

Open Access

https://doi.org/10.31344/ijhhs.v5i2.270

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Abstract

Craniosynostosis refers to skull deformities secondary to the premature closure of cranial suture. Isolated or multiple sutures craniosynostosis is more common than syndromic craniosynostosis. Deformities with synostosis are stigmatizing, and this provides a strong aesthetic indication for surgical correction in the non-syndromic group of patients. We present a case of non-syndromic sagittal synostosis in a ten months old patient underwent open surgical repair for skull deformity.International Journal of Human and Health Sciences Vol. 05 No. 02 April’21 Page: 254-257

Highlights

Craniosynostosis was described as the premature closure of cranial suture leading to skull deformities by Sommerring in 1791.1 Virchow observed in 1851 that skull growth perpendicular to the fused suture is inhibited by premature fusion.[2]
Non-syndromic craniosynostosis is more common than syndromic craniosynostosis; up to 85%
Clinical diagnosis is adequate in most cases; confirmation with imaging such as X-rays, computed tomography (CT), and threedimensional CT reconstruction is effective in delineating skull base deformity

Summary

Introduction

Craniosynostosis was described as the premature closure of cranial suture leading to skull deformities by Sommerring in 1791.1 Virchow observed in 1851 that skull growth perpendicular to the fused suture is inhibited by premature fusion.[2]. Introduction: Craniosynostosis was described as the premature closure of cranial suture leading to skull deformities by Sommerring in 1791.1 Virchow observed in 1851 that skull growth perpendicular to the fused suture is inhibited by premature fusion.[2] Compensatory growth of adjacent sutures with premature fusion affects the entire skull.[3] Craniosynostosis requires correction surgery that performed addressing the whole skull and not just the fused suture. Sagittal suture fusion has an estimated incidence of 1 in 2000, making it the commonest suture involved.[4] Non-syndromic craniosynostosis is more common than syndromic craniosynostosis; up to 85%.5 Approximately 40-60% of all craniosynostosis cases are nonsyndromic sagittal craniosynostosis; making it the most frequent variant leading to scaphocephaly.[6] Clinical diagnosis is adequate in most cases; confirmation with imaging such as X-rays, computed tomography (CT), and threedimensional CT reconstruction is effective in delineating skull base deformity. Common indications for craniosynostosis surgery are increased intracranial pressure and cosmetic deformity.

Results

Conclusion