Abstract
A Case of Intra-Abdominal Desmoplastic Small Round Cell Tumor in a Young Girl Patient
Highlights
ConclusionA Desmoplastic small round cell tumor (DSRCT) can develop at various sites, the intra-abdominal site is the most common location
Desmoplastic small round cell tumor (DSRCT) is a rare and highly aggressive mesenchymal tumor; fewer than 200 cases have been reported in the literature [1]
Case Report: We report a new case of a 16-year-old female who proceeded complaining about non-specific abdominal pain
Summary
Despite its rare incidence in women, the diagnosis of DSRCT must be considered in a young woman presenting abdominopelvic symptoms and one or more peritoneal masses. The DSRCT are characterized by a large histological polymorphism, and immunohistochemical studies and cytogenetic or molecular biology are necessary for diagnosis. The prognosis remains bleak and evolution is usually done to death, despite a heavy therapeutic care including surgery, high-dose chemotherapy and sometimes radiotherapy
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Disclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.