A case of hypertrophic cardiomyopathy with “burned-out” apex of the left ventricle due to mid-ventricular obstruction

Elena Mershina,Olga Blagova,Ekaterina Pershina,Valentin Sinitsyn

doi:10.15761/ccrr.1000s2002

Abstract

A case of hypertrophic cardiomyopathy with “burned-out” apex of the left ventricle due to mid-ventricular obstruction

Highlights

Hypertrophic cardiomyopathy (HCM) is a relatively common cardiac disease of genetic origin with incidence about 1:500 in general population
Some other atypical forms of myocardial hypertrophy and late gadolinium enhancement (LGE) patterns may be observed in HCM
This is Cardiac MRI (CMR) with LGE has an important role in differentiation of HCM from other diseases accompanied with LV myocardial hypertrophy

Summary

Introduction

Hypertrophic cardiomyopathy (HCM) is a relatively common cardiac disease of genetic origin with incidence about 1:500 in general population. Besides 3-dimensional morphological and functional analysis of the heart with very accurate grading of location and extent of myocardial hypertrophy in patients with HCM, CMR with late gadolinium enhancement (LGE) revels presence and pattern of myocardial fibrosis in the myocardium. Mershina E (2016) A case of hypertrophic cardiomyopathy with “burned-out” apex of the left ventricle due to mid-ventricular obstruction an ischemic pattern of contrast enhancement (subendocardial and transmural) of the myocardium in the apical region (Figure 3). Such type of contrast enhancement is regarded as not typical for HCM. There was a myocardial bridge over proximal segment of left anterior descending artery (LAD) (Figure 4)

Discussion

Conclusion