A Case Of Congenital Aplasia Cutis Occupying A Large Area On The Scalp

Abstract

Aplasia cutis congenita (ACC) is a rare heterogeneous group of diseases characterized by the absence of skin at birth. It affects males and females equally. It is usually located on the scalp and can be in different sizes from 0.5 up to 15 cm. Typically, it is sporadic, although hereditary cases have also been reported. In cases with bone tissue absence under the lesion, the risk of developing complications increases, and surgical intervention may be required. In this article, we presented a rare case of ACC without underlying bone tissue that covers a very large area on the scalp. In this case, the lesion epithelialized with local treatment without need for any reconstructive surgery.