A case of cochlear implantation in a patient with Paget disease

Abstract

Paget disease is a chronic osteoclastic disorder of unknown etiology that occurs most frequently in the spine, pelvis, and skull. Excessive bone resorption and consequent secondary bone formation are the main pathology associated with this condition. Paget disease is common in Europe and North America, but relatively uncommon in Asia. There is only one case report of Paget disease of temporal bone in Korea [1]. Seventy percent of Paget patients have skull lesions, and half of them have hearing impairment [2]. The type of hearing loss includes conductive, sensorineural, or mixed varieties; however, total deafness is not common. There is only one prior case report of cochlear implantation in a patient with Paget disease [3]. Here, another case of cochlear implantation in a patient with Paget disease is reported.