A Case of Bilateral Congenital Middle Ear Cholesteatoma

Abstract

The incidence of congenital middle ear cholesteatoma in children has increased recently for the following reasons：developed diagnostic instruments and increased awareness of congenital middle ear cholesteatoma. But bilateral congenital middle ear cholesteatoma is still a rare disease entity. The patient was a 3-year-old male with delayed language development. A whitish bulging mass was presented behind the anterior superior quadrant of right tympanic membrane and the left side lesion was detected on CT scan. Bilateral explotympanotomy were performed simultaneously and cholesteatomas were removed from both middle ear cavities. In the left side case, the cholesteatoma matrix was spreading diffusely and the ossiculoplasty with total ossicular replacement prosthesis was needed. There has been no evidence of recurrence up to 6 months following the surgery. We report this case with a review of literature. (Korean J Otorhinolaryngol-Head Neck Surg 2009;52:193-6)