594 A Review of Cardiac Surgical Procedures and Outcomes for Paediatric Rheumatic Heart Disease in Western Australia From 2000-2018

Abstract

Surgical intervention is an important treatment modality for advanced rheumatic heart disease (RHD). This study aimed to describe patient characteristics and outcomes from cardiac surgery for RHD in patients referred to the only tertiary paediatric hospital in Western Australia. An analysis of patient characteristics and cardiac surgery outcomes in patients with RHD was undertaken, using data from clinical cardiac databases, medical notes and correspondence from rural outreach clinics. 29 patients (58.6% female, 96.6% Aboriginal, Maori or Pacific Islander) underwent 34 cardiac surgeries for RHD between 2000-2018. Median age at first surgery was 12.2 (range 4-16) years. Severe mitral regurgitation (MR) was the most common indication for surgery (58.6%), followed by mixed mitral regurgitation/aortic regurgitation (20.7%) and severe aortic regurgitation (17.2%). Mitral valve repair was the most common operation (75.9%). 2 patients had mitral valve replacement (MVR) at first operation, 3 patients had MVR at second operation and 2 had MVR at third operation. There was no early mortality. 1 patient required early (<30 days) reoperation for aortic valve repair failure. 2 patients had late reoperations at 3.3 and 6.1 months duration for MR. 4 (14%) patients experienced ARF recurrences. Late mortality occurred in 3 (10.3%) patients, all due to cardiac causes. On last follow-up echocardiogram 5 patients (17.2%) had moderate MR and none had severe MR. This is the first study to describe characteristics and outcomes in WA paediatric patients having surgery for RHD. Outcomes are comparable to similar studies, with favourable long-term survival.