190 días de pentalogía de cantrell: reporte de caso y revisión de tema

Abstract

Cantrell Pentalogy is a rare congenital anomaly that affects the development of organs in the thorax and abdomen of a fetus, characterized by five primary defects: anterior abdominal wall defects, sternal defects, diaphragmatic defects, cardiac anomalies, and defects in other organs such as lungs, liver, kidneys, and central nervous system. It is named after the American physician Everett R. Cantrell, who first described the condition in 1958. Cantrell Pentalogy is an extremely rare and severe condition, often associated with high mortality rates due to respiratory and cardiac complications. Treatment typically involves early-life surgical repair; however, the prognosis remains guarded and depends on the severity of the defects and the presence of other associated anomalies. This case report presents the diagnosis of Cantrell Pentalogy in a female patient at birth and provides a 190-day follow-up of her condition.