سندرم فار؛ گزارش یک مورد در یک خانم 70 ساله:

Abstract

Idiopathic basal ganglia calcification (IBGC) or Fahr Syndrome is a rare disease caused by idiopathic calcification of the basal ganglia, which mainly presents as psychiatric symptoms, such as delirium, hallucination, and depression, or motor and cognitive neurological symptoms. The disease is usually accidentally diagnosed in brain computed tomography (CT) of patients with mental disorders. In this case study, a 70-year-old female patient is presented, who had referred to Peymaniyeh Hospital in Jahrom many times with complaints of dizziness, imbalance, irritability of the face, and frequent spasms of the fingers. Her medical history revealed hypertension, since several years ago, osteoporosis, hyperlipidemia, and genetic diseases of the heart and liver. Due to balance and neurological disorders, a CT scan of the patient's brain was obtained. CT scan showed calcification of the basal ganglia of the brain. To differentiate IBGC from other diseases that cause brain calcification, after CT scan, blood tests and evaluation of serum levels of the relevant indices were performed. Finally, the diagnosis of IBGC was confirmed and the patient was treated with calcitriva, calcium, and vitamin D drugs. She had improved and was discharged from the hospital after three days with prescription of oral medication. The calcification of the basal ganglia in this disease is similar to other infectious, metabolic, congenital, and etc. diseases that lead to nervous system disorders, so complete evaluations must be performed to rule out other causes in order to make a correct diagnosis and apply appropriate treatment.