Abstract
Hirayama disease (HD) is a rare neurological condition typically thought to be endemic for South Asia andJapanregion. Disease is characterized by juvenile muscular atrophy of unilateral distal upper extremity with benign course. MRI of the cervical spine is the way to confirm HD in clinically supposed case. Some typical MR-signs can be visualized in neutral position (abnormal cervical curvature, loss of attachment between the posterior dural sac and subjacent lamina, localized lower cervical cord atrophy with asymmetric spinal cord flattening and hyperintensity) and in flexion position (anterior shifting of the posterior dura and posterior epidural space enlargement). Here we describe 5 HD cases in Russian population with a detailed MRI description and MRI protocol recommendations in case of HD suspicion.
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