Оценка качества жизни детей, оперированных по поводу «суперкороткой формы» болезни Гиршпрунга

Abstract

So far, there have been very few reports on the quality of life (QoL) in children receiving treatment for Hirschsprung's disease in both Russian and foreign literature. Objective. To evaluate the QoL of children with ultrashort Hirschsprung's disease. Patients and methods. We evaluated the QoL in 203 patients with ultrashort Hirschsprung's disease. Group 1a included 119 children who underwent Linn surgery, whereas group 1b comprised 84 children who underwent posterior myectomy. Results. The preoperative QoL of children with ultrashort Hirschsprung's disease was lower than that in healthy children. In the early postoperative period, the QoL in patients was still lower than that in controls; however, it slightly increased compared to preoperative QoL. Twelve months postoperatively, patients' QoL was insignificantly lower than the QoL of healthy children, but has improved significantly compared to preoperative QoL. Conclusion. Comparison of postoperative QoL in patients with ultrashort Hirschsprung's disease showed that children in both groups demonstrated positive dynamics after surgery compared to preoperative parameters. Patients from group 1a had a more pronounced improvement in their QoL than patients from group 1b. Key words: Hirschsprung's disease, quality of life, ultrashort Hirschsprung's disease