Abstract
Mitochondrial encephalomyopathy is a multisystem disease, affecting predominantly the CNS and skeletal muscles, and is caused by defects in mitochondrial function. There are three distinctive syndromes: KSS (Kearns-Sayre syndrome), MELAS (mitochondrial myopathy, encephalomyopathy, lactic acidosis and stroke-like episodes), and MERRF (myoclonus epilepsy with ragged-red fibers).Hearing impairment is one of the symptoms of mitochondrial encephalomyopathy. There have been several reports of progressive sensorineural hearing loss in children and adults with this disease. Acute hearing loss has not however, been previously reported. Two patients with KSS and one patient with MELAS, who showed sudden onset hearing loss, are described in this paper.
Sign-in/Register to access full text options 
Talk to us
Join us for a 30 min session where you can share your feedback and ask us any queries you have
Schedule a callDisclaimer: All third-party content on this website/platform is and will remain the property of their respective owners and is provided on "as is" basis without any warranties, express or implied. Use of third-party content does not indicate any affiliation, sponsorship with or endorsement by them. Any references to third-party content is to identify the corresponding services and shall be considered fair use under The CopyrightLaw.
