КАЧЕСТВО ЖИЗНИ ДЕТЕЙ С НАСЛЕДСТВЕННЫМИ НАРУШЕНИЯМИ РАЗВИТИЯ СОЕДИНИТЕЛЬНОЙ ТКАНИ И ИХ РОДИТЕЛЕЙ В ПРОЦЕССЕ ДИНАМИЧЕСКОГО КОНТРОЛЯ В УСЛОВИЯХ ПОЛИКЛИНИКИ

Abstract

Purpose of the study. To assess the quality of life of children with hereditary disorders of connective tissue development and their parents during dynamic monitoring in a polyclinic. Material and methods. In the period from 2020 to 2023, the patients were under dispensary observation. The main group of patients (n=30) and the comparison group (n=30) are presented. At the beginning of treatment, the average age was 4.7±0.5 years. For patients of the two groups, therapeutic measures were proposed, which included back massage (ten sessions once in 4 months), electrical stimulation of the back muscles (ten sessions once in 6 months), and a physical therapy complex. Additionally, patients from the main group were prescribed sessions at the school "Posture Correction", swimming, bracing, additional physiotherapy complexes (electrical stimulation of the back – 3 courses of 10 sessions per year), back massage (10 sessions every month), diet and vitamin therapy for 3 years. The quality of life was assessed using the PedsQL questionnaire. Results. It was statistically significantly proved that during the period of dispensary observation, the patients of the main group and their parents improved physical parameters in 65.0% of cases (in the comparison group in 20.3% of cases), p=0.016; emotional parameters improved in 59.8% of cases (in the comparison group in 21.0% of cases), p=0.014. At the same time, a satisfactory muscular corset was visualized, which was confirmed by additional examination methods (electroneuromyography, stabilometry); complications from the osteoarticular system were reduced. In patients from the comparison group and their parents, the quality of life did not change statistically significantly. The patients noted hypotonia of the back muscles in 53% of cases and pain on palpation along the spine in the thoracic region in 37.3% of cases (p<0.001). Conclusions. Over time, in the main group, the number of complications from the osteoarticular system was minimized and the quality of life in patients of the main group and their parents significantly improved.