Редкий случай макулярной телеангиэктазии 1-го типа у ребенка

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Macular telangiectasia type 1 is usually characterized by a slowly progressive decrease in visual acuity in the 3–4 decade of life. Although MacTel usually manifests with a slowly progressive decrease in visual acuity in the fifth to seventh decades of life, younger patients may occasionally be diagnosed with the disease. Purpose. To present a clinical case of macular telangiectasia type 1 in an 8-year-old child. Material and methods. During a screening examination in one of the schools in the Kirovsky district of Ufa, an 8-year-old child was diagnosed with low vision in his left eye. The examination included a standard ophthalmological examination, as well as optical coherence tomography technology (Triton Topcon, Nidek Mirante, Japan). Fundus photography was performed on a Visucam fundus camera (Zeiss, Germany). Results. The left eye fundus showed microaneurysms, macular edema in the macular zone. According to OCT and OCT with laser scanning ophthalmoscopy, pathological changes in retinal structures were noted in the form of multiple cystic cavities of the neuroepithelium, deposits of small hyperreflective inclusions, intraretinal aneurysmal structures and violations of microangioarchitectonics and hypoperfusion zones. Conclusion. The clinical case demonstrates a rare form of macular telangiectasia type 1 in a child, complicated by cystic macular edema. For the diagnosis and monitoring of this disease, the use of optical coherence tomography with angio-mode is optimal, which is especially import ant when used in children. Key words: macular telangiectasia, OCT, macular edema, child