ТРУДНОСТИ РАННЕЙ ДИАГНОСТИКИ ЮВЕНИЛЬНОГО ДЕРМАТОМИОЗИТА: КРАТКИЙ ОБЗОР ЛИТЕРАТУРЫ И КЛИНИЧЕСКИЙ СЛУЧАЙ

Abstract

Juvenile dermatomyositis (JDM) is an autoimmune, relatively rare multisystem disease of unknown etiology, of which late diagnosis and late initiation of therapy can lead to a child's disability and even lethal outcome. The disease begins in most cases at the age of 5–12 years though can manifest itself both in earlier, and at more advanced age. This disease has a pronounced clinical polymorphism, which complicates early diagnosis and therapy. The article provides a brief overview of research car-ried out in recent years. A rare case of development of juvenile dermatomyositis in a teenager is con-sidered. Attention is drawn to the complexity of staging this disease during the initial treatment for medical care. A positive dynamics of the course of the disease was shown against the background of correctly selected therapy. The importance of adherence to the prescribed treatment is indicated, the refusal of which can lead to adverse outcomes