Congenital paraesophageal hernia (CPEH) is an uncommon type of diaphragmatic hernia in the paediatric age. It can be asymptomatic, present with a variety of chronic gastrointestinal and respiratory symptoms or complicated by acute gastric volvulus with strangulation in serious cases. Its rare occurrence and presentation with non-specific clinical features may delay the diagnosis. The principles of surgical treatment are generally well established with anti-reflux procedures included. Traditionally, surgery has been done using an open approach. Recently, laparoscopic repairs with encouraging outcomes have been reported. We present the case of an 18-month-old patient referred to an outpatient Clinic of Paediatric Surgery with incidental X-ray finding of CPEH type II confirmed by CT scan. The patient underwent an elective laparoscopy accompanied with Nissen fundoplication. According to our experience and literature review, we suggest laparoscopic repair of CPEH as an effective and safe method of treatment in infants and children.