An operated case of solid and cystic tumor of the pancreas is reported. A 17-year-old woman was admitted to the hospital because of a fist-sized tumor with tenderness in the left upper abdomen. Ultrasonography and computed tomography revealed a well-defined cystic tumor in the pancreatic body. On November 2nd. 1992, distal pancreatectomy with splenectomy was performed under the diagnosis of solid and cystic tumor of the pancreas. At laparotomy, the tumor was found to be well encapsulated and was 10×5.5×5cm in size. No infiltration into the surrounding tissue was noted. On the section, the tumor was composed of solid and cystic lesions with severe necrotic degeneration and hemorrhage. Microscopic findings showed the tumor cells with round nuclei and eosinophilic or clear cytoplasm proliferated in the solid nest or pseudopapillary pattern. Cystic necrosis and hemorrhage were also seen. Venous invasion was observed in the capsule. Immunohistochemically, the tumor cells were positive for cytokeratins, alpha 1-antitrypsin, neuron specific enolase, S-100 protein and vimentin. Examination for estrogen receptor was negative, but positive for progesterone receptor. Histological diagnosis was solid and cystic tumor of the pancreas.