Surgical treatment of Ebstein anomaly: A unicenter experience

Abstract

Aim: Ebstein anomaly is a rare congenital cardiac disorder that causing by failure of delamination of the tricuspid valve. Various surgical methods have been developed so far as treatment options. Our initial experience and short term follow up reported herein.Materials and Methods: Ten patients underwent surgical treatment with a diagnosis of Ebstein anomaly in our center between 2007 and 2017. Two patients underwent one and a half ventricle repair and Danielson method applied to eight patients. The X-clamping and cardiopulmonary by-pass (CPB) timing, duration in intensive care unit (ICU), extubation time and need for blood product were compared between Danielson and one and a half ventricle repair applied patients.Results: There was no mortality among patients. In the one and a half repair applied group both X-clamping (p=0.044) and CPB time (p=0.044) was longer compared to Danielson group. On the other hand there is no significantly difference between groups in ICU duration (p=0.400) or extubation timing (p=0.889). Furthermore, need for blood product and amount of drainage were not different between groups when two infant age cases were excepted while calculating. Conclusion: Danielson method is safe and effective in the repair of Ebstein anomaly and can be applied at infant age with similar clinical outcomes. Nevertheless, one and a half repair option is also beneficial in patients with a large size atrialized right ventricular volume. The last decision should be confirmed by heart team considering patient characteristics and surgeons’ past experience.