Abstract
Osteogenesis imperfecta presents with unique challenges to the anaesthetist. We report a case of osteogenesis imperfecta, posted for rush rodding of femur managed with caudal anaesthesia and sedation with dexmedetomidine and ketamine.
Highlights
Osteogenesis imperfecta (OI) is a rare connective tissue disorder caused by mutations of the collagen type I - COLIA 1 and COLIA 2 genes.[1]
We present a known case of osteogenesis imperfect posted for rush rodding of femur successfully managed using caudal anaesthesia and sedation using dexmedetomidine infusion
In view of the possible instability of cervical spine, we decided to do the case under caudal anaesthesia and sedation using dexmedetomidine and ketamine
Summary
Osteogenesis imperfecta (OI) is a rare connective tissue disorder caused by mutations of the collagen type I - COLIA 1 and COLIA 2 genes.[1]. Introduction Osteogenesis imperfecta (OI) is a rare connective tissue disorder caused by mutations of the collagen type I - COLIA 1 and COLIA 2 genes.[1] The disease is characterised by fragile bones, hyperextensible joints, blue sclera, improper dentition, and progressive hearing loss.[2] OI is classified into four types according to silence classification.[3] We present a known case of osteogenesis imperfect posted for rush rodding of femur successfully managed using caudal anaesthesia and sedation using dexmedetomidine infusion. Case report An 8-year-old boy, known patient with osteogenesis imperfecta type 1, weighing 10 kg was posted for rush rodding of femur.
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