Abstract
A 62-year-old man had arthritis and an infiltrated purpuric eruption of the legs. He presented then a cyanosis and aches of the left ear’s pinna with a voice disturbance and an inflammatory aspect of the nose. He had an anemia and a thrombopenia. The infectious and auto-immune research was negative. The laryngo-tracheal scan revealed calcifications of the larynx, the trachea and the initial portion of bronchi. Moreover, the biopsy from ear’s pinna cartilage confirmed the diagnosis of chondritis and peri-chondritis. He was thus considered to have the association with relapsing polychondritis and a myelodysplastic syndrome. The patient was treated with corticosteroids and iterative transfusions. The articular and skinny patient’s symptoms completely resolved. The anemia and the thrombopenia were partially improved. The relapsing polychondritis can be considered as paraneoplastic complication in the context of a myelodysplastic syndrome or as a fortuitous association. The mechanism of such an association remains unknown.
Highlights
The relapsing polychondritis [1] is an acquired disease of unknown etiology, chronic course, and tendency to recur
The case highlights the association between relapsing polychondritis and myelodysplastic syndrome
The diagnosis of relapsing polychondritis was confirmed in our patient by the association of four signs
Summary
The relapsing polychondritis [1] is an acquired disease of unknown etiology, chronic course, and tendency to recur. It is characterized by inflammation and degeneration of cartilage and can result in deformities such as floppy ear and saddle nose. It’s a rare inflammatory disease which can implicate organs rich of proteoglycan as the eyes, the heart, the vessels and the kidneys [2]. The case highlights the association between relapsing polychondritis and myelodysplastic syndrome (2015) Relapsing Polychondritis Associated with Myelodysplastic Syndrome.
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