Presentation of Low-grade Fibro Myxoid Sarcoma in Male Breast: Rare and Challenging Entity for Diagnosis - A Case Report with Review of Literature

Abstract

Primary breast sarcomas are very rare tumors accounting <1% of primary malignant breast tumors and <5% of soft tissue sarcomas. They are seen in young adults with tendency for multiple recurrences. They can metastasize if incompletely excised, so the prognosis is poor. There is rarity because of lack of consensus and a few case reports have been reported till date. We report a case of 31-year-old male with history of left areolar swelling. He had history of excision biopsy one year back from same site which on histopathology was diagnosed as low-grade fibro myxoid sarcoma. The patient was asymptomatic for one year and now presented with history of swelling at scar site. The lumpectomy was done. There was no systemic dissemination. The tumor was histologically diagnosed as recurrence of low-grade fibro myxoid sarcoma. We review the literature about breast sarcomas and low-grade fibro myxoid sarcoma of the breast.