Abstract
Rhabdomyosarcoma is the most common soft tissue sarcoma in children under the age of 15 years, constitutes 5% to 8% of all solid tumors in the pediatric population. The most common RMS is the embryonal subtype, followed by the alveolar subtype. The alveolar subtype typically affects older children and young adults and frequently involves the extremities and perineal sites with peak at 10-25 years. Alveolar RMS of labia majora is extremely rare.
Highlights
Rhabdomyosarcoma (RMS) is the most common soft tissue sarcoma in children under the age of 15 years, constitutes 5% to 8% of all solid tumors in the pediatric population
The vulvar site Alveolar Rhabdomyosarcoma (ARMS) is extremely rare and only a few cases have been reported in literature[3]
Gross Examination, a single nodular 3X2X1 cm size, firm grey white with presence of hemorrhagic area (0.5X0.2) and histopathology shows malignant undifferentiated cells arranged in alveolar pattern (Figure 1), Desmin positive, immunonegative for 2100, SMA, CD34 diagnosed as Alveolar Rhabdomyosarcoma
Summary
Rhabdomyosarcoma (RMS) is the most common soft tissue sarcoma in children under the age of 15 years, constitutes 5% to 8% of all solid tumors in the pediatric population. It is the third most common extracranial childhood solid tumor after neuroblastoma and Wilms’ tumor[1]. The most common RMS is the embryonal subtype, followed by the alveolar subtype. The vulvar site Alveolar Rhabdomyosarcoma (ARMS) is extremely rare and only a few cases have been reported in literature[3]. We are reporting a case of alveolar RMS of Labia Majora (Vulva) in a young girl
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