Abstract
Aim: Dermatofibrosarcoma protuberans (DFSP) is a rare skin tumor. The diagnosis is challenging because it is usually hard to differ DFSP from other skin lesions. Distant metastasis is rare, but local recurrence is common.The aim of this study is to review the treatment algorithms in DFSPs that are detected incidentally and to increase awareness about this rare tumor.
 Material and Methods: 17 patients who underwent excision of epidermal lesions which were considered to be benign and were diagnosed with DFSP, at departmant of general surgery between 2012 and 2017, were analyzed.
 Result: A total of 17 patients were analyzed retrospectively. No recurrence was detected in any of ourpatients.
 Conclusion: Awareness of this rare entity is important for diagnosis and management of the disease.
Highlights
Dermatofibrosarcoma protuberans (DFSP) is a very rare mesenchymal skin tumor
Patients were compared in terms of age, gender, tumor localization, surgical margin status, re-excision status, surgical margin status after re-excision, immunohistochemical markers, mitotic activity in 10 hpf, Ki67 proliferation index, follow-up times, whether they received radiotherapy and complications related to radiotherapy
The treatment was completed with radiotherapy in 4 patients who had positive margins after re-excision
Summary
In the latest World Health Organization (WHO) 2013 classification, these tumors were classified as moderately malignant myofibroblastic tumors [1] It was first described by Darier and Ferrand, the no men clature was made by Hoffman [2]. It constitutes less than 1% of all malignancies and approximately 1% of all soft tissue sarcomas. Congenital cases have been reported, they usually occur in the 3rd decade [8,9,10] It may have a nodular appearance, such as slow-growing hypertrophic scars, it can occur without any symptoms, such as soft tissue sarcomas. The difference between the genders is not provento be significant, there are different studies showing that women or men are slightly more common [8,12]
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