Full Mouth Dental Treatment of a Child with Congenital Lipodystrophy : A Case Report

Abstract

Background: The lipodystrophies are characterized by abnormal or degenerative conditions of the body's adipose tissue, frequently with fat accumulation in non-atrophic depots and extopic sites such as liver and muscle. It is a rare disease. The estimated worldwide prevalence is 1 in 10 million population. The disease could be classified into localized, partial and generalized lipoatrophy according to the severity. The patient with lipodystrophy also suffered from metabolic disturbances such as insulin resistance with type 2 diabetes, acanthosis nigricans, hypertriglyceridaemia, liver steatosis and hypertension. The patient with specific type lipodystrophy might have problems of mandibulo-acral dysplasia.Case report: This is a 3 year 8 months old girl who with lipodystrophy and mental retardation. She had the past medical history of gum and nasal bleeding due to liver function impairment on 2011. 02. 26. She came to our dental department on 2011. 12. 26 for full mouth dental check up. Full mouth dental treatment under general anesthesia was suggested due to the patient's behavior problem and early childhood caries. The treatment was performed on 2012. 01. 09.Discussion: In this case, the patient could not cooperate with us and could not understand us due to mental retardation, consider about her condition of severe tooth decay and medical history of liver full mouth liver function impairment, dental treatment under general anesthesia was performed.