Fístula Arterio-Portal Congênita Em Criança - Relato De Caso

Abstract

Brief Description of the Purpose of the ReportDescription of a case of congenital arterioportal fistula associated with portal vein aneurism, an unusual disease.Medical HistoryA six years old male, in a diagnostic investigation because of diarrhea, abdominal distention, malnutrition and anemia. He did an utrasound that made the diagnose, posteriorly confirmed with MRI. The child was treated with embolization, being in good clinical condition.DiagnosisCongenital arterioportal fistula.Discussion and Summary of the CaseAbnormal vascular connections within the hepatic parenchyma are unusual malformations. The patients may be symptomatics or it may be an incidental diagnosis. Arterioportal fistula is a comunication between the hepatic artery and the portal venous system, chenging the arterial flow, that goes to a focal region on a portal branch, that gets enlarged. Portal flow becomes arterialized, whit more pulsatility and the arterial flow suffers fall in its resistance index. This finds are classic and were found in this case described. On abdominal ultrasound, a cystic lesion was seen, with a "ying Yang" flow inside. MRI was performed and showed the same cystic image with flow void on T2-Weight sequences, finds that suggest vascular malformation. Clinical features asociated with this entity are portal hypertension and intestinal malabsortion, wich probably was related with this child. Liver function can declines with time. Brief Description of the Purpose of the ReportDescription of a case of congenital arterioportal fistula associated with portal vein aneurism, an unusual disease. Description of a case of congenital arterioportal fistula associated with portal vein aneurism, an unusual disease. Medical HistoryA six years old male, in a diagnostic investigation because of diarrhea, abdominal distention, malnutrition and anemia. He did an utrasound that made the diagnose, posteriorly confirmed with MRI. The child was treated with embolization, being in good clinical condition. A six years old male, in a diagnostic investigation because of diarrhea, abdominal distention, malnutrition and anemia. He did an utrasound that made the diagnose, posteriorly confirmed with MRI. The child was treated with embolization, being in good clinical condition. DiagnosisCongenital arterioportal fistula. Congenital arterioportal fistula. Discussion and Summary of the CaseAbnormal vascular connections within the hepatic parenchyma are unusual malformations. The patients may be symptomatics or it may be an incidental diagnosis. Arterioportal fistula is a comunication between the hepatic artery and the portal venous system, chenging the arterial flow, that goes to a focal region on a portal branch, that gets enlarged. Portal flow becomes arterialized, whit more pulsatility and the arterial flow suffers fall in its resistance index. This finds are classic and were found in this case described. On abdominal ultrasound, a cystic lesion was seen, with a "ying Yang" flow inside. MRI was performed and showed the same cystic image with flow void on T2-Weight sequences, finds that suggest vascular malformation. Clinical features asociated with this entity are portal hypertension and intestinal malabsortion, wich probably was related with this child. Liver function can declines with time. Abnormal vascular connections within the hepatic parenchyma are unusual malformations. The patients may be symptomatics or it may be an incidental diagnosis. Arterioportal fistula is a comunication between the hepatic artery and the portal venous system, chenging the arterial flow, that goes to a focal region on a portal branch, that gets enlarged. Portal flow becomes arterialized, whit more pulsatility and the arterial flow suffers fall in its resistance index. This finds are classic and were found in this case described. On abdominal ultrasound, a cystic lesion was seen, with a "ying Yang" flow inside. MRI was performed and showed the same cystic image with flow void on T2-Weight sequences, finds that suggest vascular malformation. Clinical features asociated with this entity are portal hypertension and intestinal malabsortion, wich probably was related with this child. Liver function can declines with time.