Dermatofibrosarcoma protuberans of the maxillofacial region: Report of a rare case and literature review

Abstract

Dermatofibrosarcoma protuberans is a low-grade malignancy that rarely occurs. When it occurs, it typically involves the trunk or extremities, but seldom occurs in the maxillofacial region. Its management in the maxillofacial region characteristically presents an esthetic challenge to the surgeon, especially because its surgical management often requires wide excision. We report a case of dermatofibrosarcoma protuberans of the lip and adjacent structures in a 42-year-old male. Wide excision of the tumor was done, and immediate reconstruction was achieved with a combination of platysma flap and Karapandzic lip reconstruction technique. The acceptable esthetic outcome was achieved, and the patient is currently being followed up. Although dermatofibrosarcoma protuberans infrequently occurs in the maxillofacial region, it may occur nonetheless; therefore, clinicians should be aware of this possibility. Surgical treatment of this tumor in the maxillofacial region often presents daunting reconstructive challenges.