A rare case of granulomatosis with polyangiitis (Wegener’s) presenting with tracheo-bronchial involvement

Abstract

Granulomatosis with polyangiitis (Wegener’s) (GPA) is a form of systemic vasculitis that involves primarily the upper and lower airways and the kidneys. Although the pulmonary involvement of GPA is well described, the lower airway findings are rarely involved, and only various descriptions have been reported. The most frequent airway manifestations include subglottic stenosis and inflammation, and tracheal and bronchial stenoses. We, hereby, report a case of GPA presenting with fever, cough and haemoptysis with bronchoscopy showing markedly inflamed bronchial mucosa.